A case of catecholaminergic polymorphic ventricular tachycardia

Seung Yul Lee, Jin Bae Kim, Eui Im, Woo In Yang, Boyoung Joung, Moon Hyoung Lee, Sung Soon Kim

Research output: Contribution to journalArticle

4 Citations (Scopus)

Abstract

Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a familial cardiac arrhythmia that is related to RYR2 or CASQ2 gene mutation. It occurs in patients with structurally normal heart and causes exercise-emotion-triggered syncope and sudden cardiac death. We experienced a case of CPVT in an 11 year-old female patient who was admitted for sudden cardiovascular collapse. The initial electrocardiogram (ECG) on emergency department revealed ventricular fibrillation. After multiple defibrillations, sinus rhythm was restored. However, recurrent ventricular fibrillation occurred during insertion of nasogastric tube without sedation in coronary care unit. On ECG monitoring, bidirectional ventricular tachycardia occurred with sinus tachycardia and then degenerated into ventricular fibrillation. To our knowledge, there has been no previous case report of CPVT triggered by sinus tachycardia in Korea. Therefore, we report the case as well as a review of the literature.

Original languageEnglish
Pages (from-to)448-451
Number of pages4
JournalYonsei medical journal
Volume50
Issue number3
DOIs
Publication statusPublished - 2009 Jul 30

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Ventricular Fibrillation
Sinus Tachycardia
Electrocardiography
Coronary Care Units
Sudden Cardiac Death
Syncope
Korea
Hospital Emergency Service
Cardiac Arrhythmias
Emotions
Exercise
Mutation
Genes
Polymorphic catecholergic ventricular tachycardia

All Science Journal Classification (ASJC) codes

  • Medicine(all)

Cite this

Lee, S. Y., Kim, J. B., Im, E., Yang, W. I., Joung, B., Lee, M. H., & Kim, S. S. (2009). A case of catecholaminergic polymorphic ventricular tachycardia. Yonsei medical journal, 50(3), 448-451. https://doi.org/10.3349/ymj.2009.50.3.448
Lee, Seung Yul ; Kim, Jin Bae ; Im, Eui ; Yang, Woo In ; Joung, Boyoung ; Lee, Moon Hyoung ; Kim, Sung Soon. / A case of catecholaminergic polymorphic ventricular tachycardia. In: Yonsei medical journal. 2009 ; Vol. 50, No. 3. pp. 448-451.
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Lee, SY, Kim, JB, Im, E, Yang, WI, Joung, B, Lee, MH & Kim, SS 2009, 'A case of catecholaminergic polymorphic ventricular tachycardia', Yonsei medical journal, vol. 50, no. 3, pp. 448-451. https://doi.org/10.3349/ymj.2009.50.3.448

A case of catecholaminergic polymorphic ventricular tachycardia. / Lee, Seung Yul; Kim, Jin Bae; Im, Eui; Yang, Woo In; Joung, Boyoung; Lee, Moon Hyoung; Kim, Sung Soon.

In: Yonsei medical journal, Vol. 50, No. 3, 30.07.2009, p. 448-451.

Research output: Contribution to journalArticle

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