A case of xanthoma disseminatum presenting as pedunculating nodules and plaques

Tag Won Kang, Soo Chan Kim

Research output: Contribution to journalArticle

5 Citations (Scopus)

Abstract

Xanthoma disseminatum is a rare mucocutaneous xanthomatosis classified as a benign form of non-Langerhans cell histiocytosis. We describe an illustrative case with extensive mucocutaneous involvement which was unresponsive to treatment. The patient presented with numerous variable-sized, yellow-brown papules and confluent plaques on the perorbital, perioral, neck, axilla, upper chest, groin, perianal, antecubital fossae and popliteal fossae including the upper respiratory tract. She was treated with oral cyclophosphamide but showed no clinical improvement. She then developed dyspnea, dysphagia and experience defecation difficulties, so was treated with palliative surgery to help relieve the symptoms.

Original languageEnglish
Pages (from-to)290-293
Number of pages4
JournalKorean Journal of Dermatology
Volume45
Issue number3
Publication statusPublished - 2007 Mar 1

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Non-Langerhans-Cell Histiocytosis
Xanthomatosis
Axilla
Defecation
Groin
Deglutition Disorders
Palliative Care
Respiratory System
Dyspnea
Cyclophosphamide
Neck
Thorax
Therapeutics

All Science Journal Classification (ASJC) codes

  • Dermatology

Cite this

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A case of xanthoma disseminatum presenting as pedunculating nodules and plaques. / Kang, Tag Won; Kim, Soo Chan.

In: Korean Journal of Dermatology, Vol. 45, No. 3, 01.03.2007, p. 290-293.

Research output: Contribution to journalArticle

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