IgG4-related sclerosing disease involving the superior vena cava and the atrial septum of the heart

Changho Song, Myoung Ju Koh, Yong Nam Yoon, Boyoung Joung, Se Hoon Kim

Research output: Contribution to journalArticle

9 Citations (Scopus)

Abstract

A 55-year-old woman presented with frequent episodes of syncope due to sinus pauses. During ambulatory Holter monitoring, atrial fibrillation and first-degree atrioventricular nodal block were observed. Magnetic resonance imaging and CT scans showed a tumor-like mass from the superior vena cava to the right atrial septum. Open chest cardiac biopsy was performed. The tumor was composed of proliferating IgG4-positive plasma cells and lymphocytes with surrounding sclerosis. The patient was diagnosed with IgG4-related sclerosing disease. Because of frequent sinus pauses and syncope, a permanent pacemaker was implanted. The cardiac mass was inoperable, but it did not progress during the one-year follow-up.

Original languageEnglish
Pages (from-to)1285-1288
Number of pages4
JournalYonsei medical journal
Volume54
Issue number5
DOIs
Publication statusPublished - 2013 Sep 1

Fingerprint

Atrial Septum
Superior Vena Cava
Syncope
Immunoglobulin G
Ambulatory Monitoring
Ambulatory Electrocardiography
Atrioventricular Block
Sclerosis
Plasma Cells
Atrial Fibrillation
Neoplasms
Thorax
Magnetic Resonance Imaging
Lymphocytes
Biopsy

All Science Journal Classification (ASJC) codes

  • Medicine(all)

Cite this

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abstract = "A 55-year-old woman presented with frequent episodes of syncope due to sinus pauses. During ambulatory Holter monitoring, atrial fibrillation and first-degree atrioventricular nodal block were observed. Magnetic resonance imaging and CT scans showed a tumor-like mass from the superior vena cava to the right atrial septum. Open chest cardiac biopsy was performed. The tumor was composed of proliferating IgG4-positive plasma cells and lymphocytes with surrounding sclerosis. The patient was diagnosed with IgG4-related sclerosing disease. Because of frequent sinus pauses and syncope, a permanent pacemaker was implanted. The cardiac mass was inoperable, but it did not progress during the one-year follow-up.",
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IgG4-related sclerosing disease involving the superior vena cava and the atrial septum of the heart. / Song, Changho; Koh, Myoung Ju; Yoon, Yong Nam; Joung, Boyoung; Kim, Se Hoon.

In: Yonsei medical journal, Vol. 54, No. 5, 01.09.2013, p. 1285-1288.

Research output: Contribution to journalArticle

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