International Bullous Diseases Group

consensus on diagnostic criteria for epidermolysis bullosa acquisita

the International Bullous Diseases Group

Research output: Contribution to journalReview article

15 Citations (Scopus)

Abstract

Background: Epidermolysis bullosa acquisita (EBA) is a complex autoimmune bullous disease disease with variable clinical presentations and multiple possible diagnostic tests, making an international consensus on the diagnosis of EBA essential. Objectives: To obtain an international consensus on the clinical and diagnostic criteria for EBA. Methods: The International Bullous Diseases Group (IBDG) met three times to discuss the clinical and diagnostic criteria for EBA. For the final voting exercise, 22 experts from 14 different countries voted on 50 different items. When > 30% disagreed with a proposal, a discussion was held and re-voting carried out. Results: In total, 48 of 50 proposals achieved consensus after discussion. This included nine diagnostic criteria, which are summarized in a flow chart. The IBDG was unable to determine one procedure that would be applicable worldwide. A limitation of the study is that differential diagnosis of bullous systemic lupus erythematosus has not been addressed. Conclusions: This first international consensus conference established generally agreed-upon clinical and laboratory criteria defining the clinical classification of and diagnostic testing for EBA. Holding these voting exercises in person with the possibility of discussion prior to voting has advantages in reaching consensus over Delphi exercises with remote voting.

Original languageEnglish
Pages (from-to)30-41
Number of pages12
JournalBritish Journal of Dermatology
Volume179
Issue number1
DOIs
Publication statusPublished - 2018 Jul 1

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Epidermolysis Bullosa Acquisita
Politics
Routine Diagnostic Tests
Systemic Lupus Erythematosus
Autoimmune Diseases
Differential Diagnosis

All Science Journal Classification (ASJC) codes

  • Dermatology

Cite this

@article{635e154d12f2443c9311470a9c66798d,
title = "International Bullous Diseases Group: consensus on diagnostic criteria for epidermolysis bullosa acquisita",
abstract = "Background: Epidermolysis bullosa acquisita (EBA) is a complex autoimmune bullous disease disease with variable clinical presentations and multiple possible diagnostic tests, making an international consensus on the diagnosis of EBA essential. Objectives: To obtain an international consensus on the clinical and diagnostic criteria for EBA. Methods: The International Bullous Diseases Group (IBDG) met three times to discuss the clinical and diagnostic criteria for EBA. For the final voting exercise, 22 experts from 14 different countries voted on 50 different items. When > 30{\%} disagreed with a proposal, a discussion was held and re-voting carried out. Results: In total, 48 of 50 proposals achieved consensus after discussion. This included nine diagnostic criteria, which are summarized in a flow chart. The IBDG was unable to determine one procedure that would be applicable worldwide. A limitation of the study is that differential diagnosis of bullous systemic lupus erythematosus has not been addressed. Conclusions: This first international consensus conference established generally agreed-upon clinical and laboratory criteria defining the clinical classification of and diagnostic testing for EBA. Holding these voting exercises in person with the possibility of discussion prior to voting has advantages in reaching consensus over Delphi exercises with remote voting.",
author = "{the International Bullous Diseases Group} and C. Prost-Squarcioni and F. Caux and E. Schmidt and Jonkman, {M. F.} and S. Vassileva and SooChan Kim and P. Iranzo and M. Daneshpazhooh and J. Terra and J. Bauer and J. Fairley and R. Hall and M. Hertl and Lehman, {J. S.} and B. Marinovic and A. Patsatsi and D. Zillikens and V. Werth and Woodley, {D. T.} and Murrell, {D. F.}",
year = "2018",
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International Bullous Diseases Group : consensus on diagnostic criteria for epidermolysis bullosa acquisita. / the International Bullous Diseases Group.

In: British Journal of Dermatology, Vol. 179, No. 1, 01.07.2018, p. 30-41.

Research output: Contribution to journalReview article

TY - JOUR

T1 - International Bullous Diseases Group

T2 - consensus on diagnostic criteria for epidermolysis bullosa acquisita

AU - the International Bullous Diseases Group

AU - Prost-Squarcioni, C.

AU - Caux, F.

AU - Schmidt, E.

AU - Jonkman, M. F.

AU - Vassileva, S.

AU - Kim, SooChan

AU - Iranzo, P.

AU - Daneshpazhooh, M.

AU - Terra, J.

AU - Bauer, J.

AU - Fairley, J.

AU - Hall, R.

AU - Hertl, M.

AU - Lehman, J. S.

AU - Marinovic, B.

AU - Patsatsi, A.

AU - Zillikens, D.

AU - Werth, V.

AU - Woodley, D. T.

AU - Murrell, D. F.

PY - 2018/7/1

Y1 - 2018/7/1

N2 - Background: Epidermolysis bullosa acquisita (EBA) is a complex autoimmune bullous disease disease with variable clinical presentations and multiple possible diagnostic tests, making an international consensus on the diagnosis of EBA essential. Objectives: To obtain an international consensus on the clinical and diagnostic criteria for EBA. Methods: The International Bullous Diseases Group (IBDG) met three times to discuss the clinical and diagnostic criteria for EBA. For the final voting exercise, 22 experts from 14 different countries voted on 50 different items. When > 30% disagreed with a proposal, a discussion was held and re-voting carried out. Results: In total, 48 of 50 proposals achieved consensus after discussion. This included nine diagnostic criteria, which are summarized in a flow chart. The IBDG was unable to determine one procedure that would be applicable worldwide. A limitation of the study is that differential diagnosis of bullous systemic lupus erythematosus has not been addressed. Conclusions: This first international consensus conference established generally agreed-upon clinical and laboratory criteria defining the clinical classification of and diagnostic testing for EBA. Holding these voting exercises in person with the possibility of discussion prior to voting has advantages in reaching consensus over Delphi exercises with remote voting.

AB - Background: Epidermolysis bullosa acquisita (EBA) is a complex autoimmune bullous disease disease with variable clinical presentations and multiple possible diagnostic tests, making an international consensus on the diagnosis of EBA essential. Objectives: To obtain an international consensus on the clinical and diagnostic criteria for EBA. Methods: The International Bullous Diseases Group (IBDG) met three times to discuss the clinical and diagnostic criteria for EBA. For the final voting exercise, 22 experts from 14 different countries voted on 50 different items. When > 30% disagreed with a proposal, a discussion was held and re-voting carried out. Results: In total, 48 of 50 proposals achieved consensus after discussion. This included nine diagnostic criteria, which are summarized in a flow chart. The IBDG was unable to determine one procedure that would be applicable worldwide. A limitation of the study is that differential diagnosis of bullous systemic lupus erythematosus has not been addressed. Conclusions: This first international consensus conference established generally agreed-upon clinical and laboratory criteria defining the clinical classification of and diagnostic testing for EBA. Holding these voting exercises in person with the possibility of discussion prior to voting has advantages in reaching consensus over Delphi exercises with remote voting.

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DO - 10.1111/bjd.16138

M3 - Review article

VL - 179

SP - 30

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JO - British Journal of Dermatology

JF - British Journal of Dermatology

SN - 0007-0963

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