Kasabach-Merritt syndrome arising from tufted angioma successfully treated with systemic corticosteroid

Taegyun Kim, Mi Ryung Roh, Soohyun Cho, Kee Yang Chung

Research output: Contribution to journalArticle

24 Citations (Scopus)

Abstract

We report a case of Kasabach-Merritt syndrome arising from a tufted angioma successfully treated with systemic corticosteroid. A 2-month-old male infant presented with a palm-sized, erythematous induration on his left pubis. The lesion was diagnosed as tufted angioma histopathologically. After 1 month, the lesion suddenly expanded to the abdomen and scrotum. Initial laboratory tests were consistent with consumptive coagulopathy. He was diagnosed with Kasabach-Merritt syndrome and treated with intravenous dexamethasone at 0.32 mg/kg/day (equivalent to prednisolone 2.0 mg/kg/day). Two days after initiating the treatment, his platelet counts recovered and the lesion ceased to expand. Steroid therapy was converted to oral prednisolone and the dosage was subsequently tapered, and the lesion gradually involuted with no signs of recurrence for a year.

Original languageEnglish
Pages (from-to)426-430
Number of pages5
JournalAnnals of Dermatology
Volume22
Issue number4
DOIs
Publication statusPublished - 2010 Nov

All Science Journal Classification (ASJC) codes

  • Dermatology

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