Schilder's disease in a young child with tumefactive demyelinating brain lesion

Hyo Jeong Kim, Sang Mi Lee, HeungDong Kim, Joon Soo Lee, hoonchul kang

Research output: Contribution to journalArticle

Abstract

Schilder's disease is a rare sporadic demyelinating disease of the brain. We report a girl with Schilder's disease who had undergone Kasai operation for biliary atresia. The patient presented with acute right hemiparesis. Brain magnetic resonance imaging (MRI) showed a single large tumefactive white matter lesion. A diagnosis of Schilder's disease was based on clinical features and MRI findings. The patient showed dramatic clinical improvement and significant regression of the lesion in response to high-dose intravenous methyl prednisone, and remained free of relapse of other neurologic problems during the 3-year follow-up.

Original languageEnglish
Pages (from-to)419-421
Number of pages3
JournalNeurology Asia
Volume18
Issue number4
Publication statusPublished - 2013 Dec 1

Fingerprint

Diffuse Cerebral Sclerosis of Schilder
Brain
Magnetic Resonance Imaging
Biliary Atresia
Demyelinating Diseases
Paresis
Prednisone
Nervous System
Recurrence

All Science Journal Classification (ASJC) codes

  • Neurology
  • Clinical Neurology

Cite this

Kim, Hyo Jeong ; Lee, Sang Mi ; Kim, HeungDong ; Lee, Joon Soo ; kang, hoonchul. / Schilder's disease in a young child with tumefactive demyelinating brain lesion. In: Neurology Asia. 2013 ; Vol. 18, No. 4. pp. 419-421.
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Schilder's disease in a young child with tumefactive demyelinating brain lesion. / Kim, Hyo Jeong; Lee, Sang Mi; Kim, HeungDong; Lee, Joon Soo; kang, hoonchul.

In: Neurology Asia, Vol. 18, No. 4, 01.12.2013, p. 419-421.

Research output: Contribution to journalArticle

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