Schilder's disease in a young child with tumefactive demyelinating brain lesion

Hyo Jeong Kim, Sang Mi Lee, Heung Dong Kim, Joon Soo Lee, Hoon Chul Kang

Research output: Contribution to journalArticle

1 Citation (Scopus)


Schilder's disease is a rare sporadic demyelinating disease of the brain. We report a girl with Schilder's disease who had undergone Kasai operation for biliary atresia. The patient presented with acute right hemiparesis. Brain magnetic resonance imaging (MRI) showed a single large tumefactive white matter lesion. A diagnosis of Schilder's disease was based on clinical features and MRI findings. The patient showed dramatic clinical improvement and significant regression of the lesion in response to high-dose intravenous methyl prednisone, and remained free of relapse of other neurologic problems during the 3-year follow-up.

Original languageEnglish
Pages (from-to)419-421
Number of pages3
JournalNeurology Asia
Issue number4
Publication statusPublished - 2013 Dec 1

All Science Journal Classification (ASJC) codes

  • Neurology
  • Clinical Neurology

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