Vulvar epithelioid sarcoma: A case report with literature review

Joseph J. Noh, Jung eun Jeon, Hera Jung, Hyun Soo Kim, Yoo Young Lee, Chel Hun Choi, Jeong Won Lee

Research output: Contribution to journalArticlepeer-review

4 Citations (Scopus)


Objective: To report a case of vulvar epithelioid sarcoma, a rare type of tumor that has been reported in 37 cases in the English literature to date. Case report: We report three cases of vulvar epithelioid sarcoma, proximal type. Wide excisions of the mass were performed with margins free of tumor in all three cases. Conclusion: Due to its low incidence, there are no evidence-based diagnostic algorithms or published recommendations for treatment. Locoregional lymph node involvement, vascular invasion, tumor size larger than 2 cm, deep localization, presence of necrosis, and a high mitotic index are known as poor prognostic factors. Adjuvant radiotherapy is advisable in the presence of a high-grade tumor or positive margins. The beneficial effect of adjuvant chemotherapy is not well established. Treatment decisions should be made based on the individual case presentation and pathology evaluation.

Original languageEnglish
Pages (from-to)132-135
Number of pages4
JournalTaiwanese Journal of Obstetrics and Gynecology
Issue number1
Publication statusPublished - 2021 Jan

Bibliographical note

Publisher Copyright:
© 2021

All Science Journal Classification (ASJC) codes

  • Obstetrics and Gynaecology


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